Last update:

   01-Feb-2021
 

Arch Hellen Med, 38(1), January-February 2021, 95-98

CASE REPORT

Scimitar syndrome in an adult presenting with effort-induced dyspnea
Α missed diagnosis

G. Michas,1 M. Pantziara-Skapoullis,2 Y. Herodotou,3 L.E. Mitselos,4 C. Christou,5 M. Soteriou,6 P. Mavrommatis7
1Medical School, University of Nicosia, Nicosia, Cyprus
2Department of Radiology, German Oncology Center, Limassol, Cyprus
3Department of Medicine, School of Health Sciences, National and Kapodistrian University of Athens, Athens, Greece
4Department of Radiology, American Medical Center, Nicosia, Cyprus
5Department of Cardiology, American Medical Center, Nicosia, Cyprus
6Department of Cardiothoracic Surgery, American Medical Center, Nicosia, Cyprus
7Cardiac Care Centre, Paphos, Cyprus

Scimitar syndrome is a rare congenital constellation of cardio-pulmonary anomalies, classically described as an association of partial anomalous pulmonary venous return, hypoplasia of the right lung and cardiac dextroposition. The case is described of a patient with the adult form of the syndrome, with partial anomalous pulmonary venous return to the inferior vena cava and a hypoplastic right lung that had evaded diagnosis for years and was eventually successfully treated surgically.

Key words: Computed tomography, Scimitar syndrome, Transesophageal echocardiography, Transthoracic echocardiography, X-ray.


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